It is fairly rare, occuring in about 1 in 2,000-5,000 live births, although it is estimated that approximately 99% of eggs with a single X chromosome will result in a miscarriage. In addition, the symptoms can be subtle and often are not noticed until the patient is near adulthood. These include short stature, swelling, a broad chest, a low hairline, low set ears and a webbed neck. Patients also do not develop ovaries and are sterile,